LymphedemaV1, Main, Exploration, bibRecord, 000B41

Secondary hypogammaglobulinemia in Waldmann's disease treated with subcutaneous immunoglobulins.

Identifieur interne : 000B41 ( Main/Exploration ); précédent : 000B40; suivant : 000B42

Secondary hypogammaglobulinemia in Waldmann's disease treated with subcutaneous immunoglobulins.

Auteurs : G. Patuzzo [Italie] ; E. Tinazzi [Italie] ; M. Micheletti [Italie] ; A. Puccetti [Italie] ; C. Lunardi [Italie]

Source :

European annals of allergy and clinical immunology [ 1764-1489 ] ; 2016.

RBID : pubmed:26934740

Descripteurs français

KwdFr :
- Adulte, Agammaglobulinémie (), Agammaglobulinémie (diagnostic), Agammaglobulinémie (immunologie), Facteurs immunologiques (administration et posologie), Facteurs immunologiques (sang), Humains, Immunoglobuline G (administration et posologie), Immunoglobuline G (sang), Indice de gravité médicale, Lymphangiectasie intestinale (), Lymphangiectasie intestinale (diagnostic), Lymphangiectasie intestinale (immunologie), Lymphoedème (), Lymphoedème (diagnostic), Lymphoedème (immunologie), Mâle, Perfusions sous-cutanées, Régime pauvre en graisses, Résultat thérapeutique, Triglycéride (administration et posologie).
MESH :
- administration et posologie : Facteurs immunologiques, Immunoglobuline G, Triglycéride.
- diagnostic : Agammaglobulinémie, Lymphangiectasie intestinale, Lymphoedème.
- immunologie : Agammaglobulinémie, Lymphangiectasie intestinale, Lymphoedème.
- sang : Facteurs immunologiques, Immunoglobuline G.
- Adulte, Agammaglobulinémie, Humains, Indice de gravité médicale, Lymphangiectasie intestinale, Lymphoedème, Mâle, Perfusions sous-cutanées, Régime pauvre en graisses, Résultat thérapeutique.

English descriptors

KwdEn :
- Adult, Agammaglobulinemia (diagnosis), Agammaglobulinemia (immunology), Agammaglobulinemia (therapy), Diet, Fat-Restricted, Humans, Immunoglobulin G (administration & dosage), Immunoglobulin G (blood), Immunologic Factors (administration & dosage), Immunologic Factors (blood), Infusions, Subcutaneous, Lymphangiectasis, Intestinal (complications), Lymphangiectasis, Intestinal (diagnosis), Lymphangiectasis, Intestinal (immunology), Lymphangiectasis, Intestinal (therapy), Lymphedema (complications), Lymphedema (diagnosis), Lymphedema (immunology), Lymphedema (therapy), Male, Severity of Illness Index, Treatment Outcome, Triglycerides (administration & dosage).
MESH :
- chemical , administration & dosage : Immunoglobulin G, Immunologic Factors, Triglycerides.
- chemical , blood : Immunoglobulin G, Immunologic Factors.
- complications : Lymphangiectasis, Intestinal, Lymphedema.
- diagnosis : Agammaglobulinemia, Lymphangiectasis, Intestinal, Lymphedema.
- immunology : Agammaglobulinemia, Lymphangiectasis, Intestinal, Lymphedema.
- therapy : Agammaglobulinemia, Lymphangiectasis, Intestinal, Lymphedema.
- Adult, Diet, Fat-Restricted, Humans, Infusions, Subcutaneous, Male, Severity of Illness Index, Treatment Outcome.

Abstract

Primary intestinal lymphangiectasia (PIL) is rare disorder characterized by congenital malformation or obstruction of intestinal lymphatic drainage; it is responsible for protein losing enteropathy leading to lymphopenia, hypoalbuminemia and hypogammaglobulinemia. A low-fat diet associated with medium-chain triglyceride supplementation is the cornerstone of PIL management. The administration of intravenous immunoglobulins does not always lead to satisfactory plasma levels and therefore the replacement therapy with immunoglobulins is controversial. We describe here the case of a patient with PIL and severe hypogammaglobulinemia treated with immunoglobulins. The striking aspect of this case is the clinical and serological benefit obtained with the subcutaneous compared to the intravenous immunoglobulins administration.

PubMed: 26934740

Affiliations:

Le document en format XML

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<affiliation wicri:level="1"><nlm:affiliation>Clinical Immunology and Allergy Unit Department of Medicine University of Verona 37134 Verona, Italy. E-mail: jeps.pz@gmail.com Phone: +39 045 812 4401 Fax: +39 045 802 7473.</nlm:affiliation>
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<term>Agammaglobulinemia (diagnosis)</term>
<term>Agammaglobulinemia (immunology)</term>
<term>Agammaglobulinemia (therapy)</term>
<term>Diet, Fat-Restricted</term>
<term>Humans</term>
<term>Immunoglobulin G (administration & dosage)</term>
<term>Immunoglobulin G (blood)</term>
<term>Immunologic Factors (administration & dosage)</term>
<term>Immunologic Factors (blood)</term>
<term>Infusions, Subcutaneous</term>
<term>Lymphangiectasis, Intestinal (complications)</term>
<term>Lymphangiectasis, Intestinal (diagnosis)</term>
<term>Lymphangiectasis, Intestinal (immunology)</term>
<term>Lymphangiectasis, Intestinal (therapy)</term>
<term>Lymphedema (complications)</term>
<term>Lymphedema (diagnosis)</term>
<term>Lymphedema (immunology)</term>
<term>Lymphedema (therapy)</term>
<term>Male</term>
<term>Severity of Illness Index</term>
<term>Treatment Outcome</term>
<term>Triglycerides (administration & dosage)</term>
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<term>Agammaglobulinémie ()</term>
<term>Agammaglobulinémie (diagnostic)</term>
<term>Agammaglobulinémie (immunologie)</term>
<term>Facteurs immunologiques (administration et posologie)</term>
<term>Facteurs immunologiques (sang)</term>
<term>Humains</term>
<term>Immunoglobuline G (administration et posologie)</term>
<term>Immunoglobuline G (sang)</term>
<term>Indice de gravité médicale</term>
<term>Lymphangiectasie intestinale ()</term>
<term>Lymphangiectasie intestinale (diagnostic)</term>
<term>Lymphangiectasie intestinale (immunologie)</term>
<term>Lymphoedème ()</term>
<term>Lymphoedème (diagnostic)</term>
<term>Lymphoedème (immunologie)</term>
<term>Mâle</term>
<term>Perfusions sous-cutanées</term>
<term>Régime pauvre en graisses</term>
<term>Résultat thérapeutique</term>
<term>Triglycéride (administration et posologie)</term>
</keywords>
<keywords scheme="MESH" type="chemical" qualifier="administration & dosage" xml:lang="en"><term>Immunoglobulin G</term>
<term>Immunologic Factors</term>
<term>Triglycerides</term>
</keywords>
<keywords scheme="MESH" type="chemical" qualifier="blood" xml:lang="en"><term>Immunoglobulin G</term>
<term>Immunologic Factors</term>
</keywords>
<keywords scheme="MESH" qualifier="administration et posologie" xml:lang="fr"><term>Facteurs immunologiques</term>
<term>Immunoglobuline G</term>
<term>Triglycéride</term>
</keywords>
<keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Lymphangiectasis, Intestinal</term>
<term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnosis" xml:lang="en"><term>Agammaglobulinemia</term>
<term>Lymphangiectasis, Intestinal</term>
<term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnostic" xml:lang="fr"><term>Agammaglobulinémie</term>
<term>Lymphangiectasie intestinale</term>
<term>Lymphoedème</term>
</keywords>
<keywords scheme="MESH" qualifier="immunologie" xml:lang="fr"><term>Agammaglobulinémie</term>
<term>Lymphangiectasie intestinale</term>
<term>Lymphoedème</term>
</keywords>
<keywords scheme="MESH" qualifier="immunology" xml:lang="en"><term>Agammaglobulinemia</term>
<term>Lymphangiectasis, Intestinal</term>
<term>Lymphedema</term>
</keywords>
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<term>Immunoglobuline G</term>
</keywords>
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<term>Lymphangiectasis, Intestinal</term>
<term>Lymphedema</term>
</keywords>
<keywords scheme="MESH" xml:lang="en"><term>Adult</term>
<term>Diet, Fat-Restricted</term>
<term>Humans</term>
<term>Infusions, Subcutaneous</term>
<term>Male</term>
<term>Severity of Illness Index</term>
<term>Treatment Outcome</term>
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<term>Agammaglobulinémie</term>
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<term>Indice de gravité médicale</term>
<term>Lymphangiectasie intestinale</term>
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<term>Mâle</term>
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<term>Régime pauvre en graisses</term>
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<front><div type="abstract" xml:lang="en">Primary intestinal lymphangiectasia (PIL) is rare disorder characterized by congenital malformation or obstruction of intestinal lymphatic drainage; it is responsible for protein losing enteropathy leading to lymphopenia, hypoalbuminemia and hypogammaglobulinemia. A low-fat diet associated with medium-chain triglyceride supplementation is the cornerstone of PIL management. The administration of intravenous immunoglobulins does not always lead to satisfactory plasma levels and therefore the replacement therapy with immunoglobulins is controversial. We describe here the case of a patient with PIL and severe hypogammaglobulinemia treated with immunoglobulins. The striking aspect of this case is the clinical and serological benefit obtained with the subcutaneous compared to the intravenous immunoglobulins administration.</div>
</front>
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<affiliations><list><country><li>Italie</li>
</country>
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<tree><country name="Italie"><noRegion><name sortKey="Patuzzo, G" sort="Patuzzo, G" uniqKey="Patuzzo G" first="G" last="Patuzzo">G. Patuzzo</name>
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<name sortKey="Lunardi, C" sort="Lunardi, C" uniqKey="Lunardi C" first="C" last="Lunardi">C. Lunardi</name>
<name sortKey="Micheletti, M" sort="Micheletti, M" uniqKey="Micheletti M" first="M" last="Micheletti">M. Micheletti</name>
<name sortKey="Puccetti, A" sort="Puccetti, A" uniqKey="Puccetti A" first="A" last="Puccetti">A. Puccetti</name>
<name sortKey="Tinazzi, E" sort="Tinazzi, E" uniqKey="Tinazzi E" first="E" last="Tinazzi">E. Tinazzi</name>
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Serveur d'exploration sur le lymphœdème

Secondary hypogammaglobulinemia in Waldmann's disease treated with subcutaneous immunoglobulins.

Secondary hypogammaglobulinemia in Waldmann's disease treated with subcutaneous immunoglobulins.

Source :

Descripteurs français

English descriptors

Abstract

Links toward previous steps (curation, corpus...)

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